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VOLUME 11 , ISSUE 4 ( July, 2010 ) > List of Articles

RESEARCH ARTICLE

Hereditary Opalescent Dentin: A Report of Two Cases

Siddharth Gupta, Rahul R. Bhowate, Ashok Bhati

Citation Information : Gupta S, Bhowate RR, Bhati A. Hereditary Opalescent Dentin: A Report of Two Cases. J Contemp Dent Pract 2010; 11 (4):49-55.

DOI: 10.5005/jcdp-11-4-49

License: CC BY-NC 3.0

Published Online: 01-07-2010

Copyright Statement:  Copyright © 2010; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Aim

The aim of this case report is to present the clinical and radiographic findings of hereditary opalescent dentin to facilitate an early diagnosis.

Background

Hereditary opalescent dentin (or dentinogenesis imperfecta) may manifest itself in three variations: i.e., Shields type I, Shields type II, and Shields type III. Dentinogenesis imperfecta occurs as an autosomal dominant trait with variable expressivity, either in presence with osteogenesis imperfecta or as a separate clinical entity in persons who have none of the features of osteogenesis imperfecta.

Case Descriptions

A seven-year old boy and his mother were both diagnosed with hereditary opalescent dentin. A review of the family dental history revealed that this condition affected not only the child's mother but his maternal grandfather and great grandfather. Both the son and the mother exhibited the same clinical and radiologic features as those reported previously with no evidence of osteogenesis imperfecta.

Summary

Being an autosomal disease, hereditary opalescent dentin runs in the family and can affect both the deciduous and permanent dentitions as a dominant trait.

Clinical Significance

Once a patient is diagnosed with hereditary opalescent dentin, other family members should be evaluated given the condition is hereditary.

Citation

Gupta S, Bhowate RR, Bhati A. Hereditary Opalescent Dentin: A Report of Two Cases. J Contemp Dent Pract [Internet]. 2010 July; 11(4):049-055. Available from: http://www. thejcdp.com/journal/view/volume11-issue4-gupta


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  1. An unusual presentation of opalescent dentin and Brandywine isolate hereditary opalescent dentin in an Ashkenazic Jewish family. Oral Surg Oral Med Oral Pathol. 1985;59(6):608-15.
  2. Dentinogenesis imperfecta type II: an affected family saga. J Oral Sci. 2007; 49(3):241-4.
  3. Hereditary opalescent dentine: variation in expression. ASDC J Dent Child. 1991;58(2):134-9.
  4. Phenotypic variation in dentinogenesis imperfecta/dentin dysplasia linked to 4q21. J Dent Res. 2006;85(4):329-33.
  5. Radiological features of hereditary opalescent dentin. Dentomaxillofac Radiol. 1998; 27(4):251-3.
  6. Inherited defects in tooth structure. Birth Defects Orig Artic Ser. 1971; 7(7):153-84.
  7. A proposed classification for heritable human dentine defects with a description of a new entity. Arch Oral Biol. 1973;18(4):543-53.
  8. Odontogenic diseases. In: Lynch MA, Brightman VJ, Greenberg MS, editors. Burket's oral medicine: diagnosis and treatment. 8th ed. Philadelphia: J.B. Lippincott Co.; 1984. p. 543-8.
  9. A textbook of oral pathology. 4th ed. Philadelphia: WB Saunders Co.; 2000. p. 58-61.
  10. Oral and maxillofacial pathology. 2nd ed. Philadelphia: Saunders; 2000. p. 94-6.
  11. Oral radiology: principles and interpretation. 5th ed. St. Louis: Mosby; 2004. p. 346-7.
  12. Dentinogenesis imperfecta type III with enamel and cementum defects. Oral Surg Oral Med Oral Pathol. 1985; 59(5):505-10.
  13. Dentinogenesis imperfe ta. An integrated conservative approach to treatment. Br Dent J. 1982;152:15-8.
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