The Journal of Contemporary Dental Practice

Register      Login

SEARCH WITHIN CONTENT

FIND ARTICLE

Volume / Issue

Online First

Archive
Related articles

VOLUME 15 , ISSUE 6 ( November-December, 2014 ) > List of Articles

CASE REPORT

Hypohidrotic Ectodermal Dysplasia: A Clinical Case with a Longitudinal Approach

Fabian Calixto Fraiz, Renato Cordeiro Gugisch, Bianca Lopes Cavalcante-Leão, Liliane Moreira Macedo

Citation Information : Fraiz FC, Gugisch RC, Cavalcante-Leão BL, Macedo LM. Hypohidrotic Ectodermal Dysplasia: A Clinical Case with a Longitudinal Approach. J Contemp Dent Pract 2014; 15 (6):788-791.

DOI: 10.5005/jp-journals-10024-1619

Published Online: 01-12-2014

Copyright Statement:  Copyright © 2014; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Aim

This paper describes a clinical case of a male with hypohidrotic ectodermal dysplasia submitted to rehabilitation and occlusal dental interventions with follow-up from 3 to 14 years of age.

Background

Due to the severe effects on function and esthetics, the clinical manifestations of ectodermal dysplasia exert a negative impact on quality of life. However, oral rehabilitation in childhood poses a challenge due to growth and development.

Case description

A male with hypohidrotic ectodermal dysplasia began dental intervention at the age of 3 years. The clinical and radiographic exams revealed the absence of several primary and permanent teeth and abnormal shape of the primary maxillary incisors. The facial characteristics were compatible with hypohidrotic ectodermal dysplasia, such as a prominent brow, everted lips, flattened bridge of the nose and small vertical facial height. The treatment proposed involved rehabilitation through successive temporary partial dentures, functional orthopedics of the jaws, esthetic reconstruction of the anterior teeth, timely occlusal intervention and preventive actions for the control of dental caries and plaque.

Conclusion

The present case demonstrates that early care plays a fundamental role in minimizing the biopsychosocial consequences of hypohidrotic ectodermal dysplasia and preparing the patient for future oral rehabilitation.

Clinical significance

Although, the literature offers a number of papers describing dental treatment for ectodermal dysplasia, few cases include long-term follow-up and the use of a functional orthopedic appliance in combination with removable dentures in such patients.

How to cite this article

Fraiz FC, Gugisch RC, Cavalcante- Leão BL, Macedo LM. Hypohidrotic Ectodermal Dysplasia: A Clinical Case with a Longitudinal Approach. J Contemp Dent Pract 2014;15(6):788-791.


PDF Share
  1. Ectodermal dysplasias. Hum Hered 1971;21(4):309-312.
  2. Prosthodontic management of ectodermal dysplasia: a review of the literature. J Prosthet Dent 1996;76(5):541-545.
  3. Ectodermal dysplasias: a clinical classification and a causal review. Am J Med Gent 1994;53(2):153-162.
  4. Simultaneous functional and fixed appliance therapy for growth modification and dental alignment prior to prosthetic habilitation in hypohidrotic ectodermal dysplasia: a clinical report. J Prosthet Dent 2004 Nov;92(5):428-433.
  5. Characterization of the face in hypohidrotic ectodermal dysplasia by cephalometric and anthropometric analysis. Birth Defects Orig Artic Ser 1988;24(2):197-203.
  6. Noninvasive longitudinal assessment of facial growth in children and adolescents with hypohidrotic ectodermal dysplasia. Eur J Oral Sci 2008;116(4):305-311.
  7. Craniofacial growth in ectodermal dysplasia. An 8 years longitudinal evaluation of Italian subjects. Angle Orthodontist 2010;80(4):733-739.
  8. Treatment outcomes for adolescent ectodermal dysplasia patients treated with dental implants. Int J Paediatr Dent 2005;15(4):241-248.
  9. Early prosthetic treatment of patients with ectodermal dysplasia: a clinical report. J Prosthet Dent 2005;93(5):419-424.
  10. Treatment of severe hypodontia-oligodontia—an interdisciplinary concept. Int J Oral Maxillofac Surg 2007;36(6):473-480.
  11. Effect of complete dentures on craniofacial growth of an ectodermal dysplasia patient: a clinical report. J Prosthont 2013;22(6):495-500.
  12. Growth analysis of a patient with ectodermal dysplasia treated with endosseous implants: 6-year follow-up. J Oral Rehabil 2006;33(3):175-182.
  13. Dental management of ectodermal dysplasia: two clinical case reports. J Dent Res Dent Clin Dent Prospect 2012;6(3):108-112.
  14. Analysis of facial growth in subjects with syndromic ectodermal dysplasia: a longitudinal analysis. Orthod Craniofac Res 2002;5(2):71-84.
  15. Treatment considerations for a patient with hypohidrotic ectodermal dysplasia: a case report. J Contemp Dent Pract 2008 March;9(3):128-134.
PDF Share

© Jaypee Brothers Medical Publishers (P) LTD.