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VOLUME 13 , ISSUE 1 ( January-February, 2012 ) > List of Articles

CASE REPORT

Juvenile Scleredema of Buschke

J Dhanuja Rani, Suneel G Patil, ST Srinivas Murthy, Ajit V Koshy, Deepak Nagpal, Sheeba Gupta

Citation Information : Rani JD, Patil SG, Murthy SS, Koshy AV, Nagpal D, Gupta S. Juvenile Scleredema of Buschke. J Contemp Dent Pract 2012; 13 (1):111-114.

DOI: 10.5005/jp-journals-10024-1104

Published Online: 01-02-2012

Copyright Statement:  Copyright © 2012; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Aim

To recognize a line of treatment for scleredema of Buschke in an adolescent.

Background

Scleredema of Buschke is an uncommon disorder characterized by induration of the skin, which includes a non pitting hardening of the skin around the neck, shoulders, and trunk sometimes the face. Three variants are recognized. The histopathologic features of scleredema are characterized by thickened collagen bundles within the reticular dermis that are separated by mucin containing fenestrations. No consistent treatment modality is currently followed.

Case report

The present case report describes scleredema of Buschke in a 10-year-old female child reported with stiffness of facial skin and difficulty in opening the mouth. The patient was treated with antibiotics and vitamin supplements and there was drastic improvement with decrease in skin stiffness and increase in mouth opening. The stiffness of facial muscles decreased and mouth opening increased.

Conclusion

Multiple treatment modalities for scleredema have been used. In the present case, high-dose antibiotic therapy was used with good prognosis.

Clinical significance

High-dose antibiotic therapy can be used for treatment of dermatologic disorders with reasonably good prognosis.

How to cite this article

Rani JD, Patil SG, Murthy STS, Koshy AV, Nagpal D, Gupta S. Juvenile Scleredema of Buschke. J Contemp Dent Pract 2012;13(1):111-114.


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